神经系统和肌肉遗传性疾病中的细胞放射敏感性研究。
Studies of cellular radiosensitivity in hereditary disorders of nervous system and muscle.
作者信息
Brennan S, Lewis P D
出版信息
J Neurol Neurosurg Psychiatry. 1983 Dec;46(12):1143-5. doi: 10.1136/jnnp.46.12.1143.
Abstract
Skin fibroblasts from patients with familial dysautonomia, Duchenne muscular dystrophy and Charcot-Marie-Tooth disease show normal sensitivity to ionising radiation, as measured by post-irradiation clonal growth. Previous reports of cellular hypersensitivity to ionising radiation and other DNA-damaging agents in familial dysautonomia and Duchenne muscular dystrophy have not been confirmed.
摘要
通过照射后克隆生长测定，家族性自主神经功能异常、杜氏肌营养不良症和夏科-马里-图斯病患者的皮肤成纤维细胞对电离辐射表现出正常的敏感性。先前关于家族性自主神经功能异常和杜氏肌营养不良症中细胞对电离辐射及其他DNA损伤剂过敏的报道尚未得到证实。
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