Böhm W, Göretzlehner G
Zentralbl Gynakol. 1983;105(24):1553-60.
The entity includes the Turner syndrome, the pure gonadal dysgenesis (Swyer syndrome), the asymmetrical gonadal differentiation, and gonadal dysgenesis of some forms of trisomy. The necessity of prophylactic gonadectomy in all patients with Y chromosome is stressed because of a close association with the arising of tumors in the dysgenetic gonads. The requirements are described of a successful substitution with steroids.
该实体包括特纳综合征、单纯性腺发育不全（斯维尔综合征）、不对称性腺分化以及某些三体形式的性腺发育不全。强调了对所有具有Y染色体的患者进行预防性性腺切除术的必要性，因为这与发育异常的性腺中肿瘤的发生密切相关。描述了成功用类固醇替代的要求。
