Shiina A, Seward J B, Edwards W D, Hagler D J, Tajik A J
J Am Coll Cardiol. 1984 Feb;3(2 Pt 1):356-70. doi: 10.1016/s0735-1097(84)80020-0.
This report details the two-dimensional echocardiographic assessment of 41 patients with Ebstein's anomaly. The anatomic spectrum of Ebstein's anomaly is correlated with surgical and autopsy observations in 66% of these patients. Morphologic abnormalities of the tricuspid valve and right heart structures were uniquely assessed by noninvasive two-dimensional echocardiographic examination. Features of the tricuspid valve that best related to decreased functional capacity were: 1) absence of the septal leaflet, and 2) pronounced tethering, restriction of motion and displacement of the anterior leaflet of the tricuspid valve. This 4 1/2 year experience suggests that two-dimensional echocardiography can replace angiography as the procedure of choice for diagnostic and morphologic assessment of Ebstein's anomaly. Cardiac catheterization is necessary only when specific hemodynamic questions or clinical inconsistencies exist.
本报告详细介绍了对41例埃布斯坦畸形患者的二维超声心动图评估。在这些患者中，66%的埃布斯坦畸形解剖谱与手术及尸检观察结果相关。通过无创二维超声心动图检查对三尖瓣和右心结构的形态学异常进行了独特评估。与功能能力下降最相关的三尖瓣特征为：1）隔叶缺失；2）三尖瓣前叶明显的腱索附着、活动受限和移位。这4年半的经验表明，二维超声心动图可取代血管造影术，成为埃布斯坦畸形诊断和形态学评估的首选检查方法。仅在存在特定血流动力学问题或临床不一致情况时才需要进行心导管检查。
