Miura T, Nakamura R, Suzuki M, Kanie J
J Hand Surg Br. 1984 Jun;9(2):153-5.
Thirty-three patients with congenital radio-ulnar synostosis were examined. There was one familial predisposition. Chromosomal patterns were examined in seventeen patients and were normal. Bone maturation appeared normal. The radial deviation angle, in the patients whose distal radial epiphysis had closed, was elevated (Madelung's deformity). However, in the patients whose distal epiphysis maturation score was 8, it was not elevated. On the other hand, elongation of the ulna (plus variant) and/or dorsal dislocation of the distal end of the ulna was seen in early life. In terms of treatment, all attempts to divide the two bones failed. It was found that derotation of the nonwriting hand by an osteotomy through the proximal fusion mass was a useful procedure.
对33例先天性桡尺骨融合患者进行了检查。有1例存在家族易感性。对17例患者的染色体模式进行了检查，结果正常。骨成熟情况看起来正常。在桡骨远端骨骺已闭合的患者中，桡偏角升高（马德隆畸形）。然而，在远端骨骺成熟评分为8分的患者中，该角度并未升高。另一方面，尺骨延长（加变异型）和/或尺骨远端背侧脱位在早期即可出现。在治疗方面，所有分离两根骨头的尝试均失败。发现通过近端融合块进行截骨术对非优势手进行去旋转是一种有效的方法。
