Noble K G, Carr R E
Am J Ophthalmol. 1978 Jul;86(1):65-75. doi: 10.1016/0002-9394(78)90017-x.
We studied four patients with peripapillary pigmentary retinal degeneration, an asymptomatic disorder that was probably benign and nonprogressive. The ophthalmoscopic appearance showed a segmental, grayish metallic sheen in association with bone spicule pigmentation, which radiated from the disk along the temporal vessel arcades and joined temporal to the macula. The optic disk, retinal vessels, periphery, and macula were normal in all patients. Visual function tests and fluorescein angiography indicated a segmental disease of the retinal pigment epithelium-photoreceptor complex.
我们研究了4例患有视乳头周围视网膜色素变性的患者，这是一种无症状的疾病，可能为良性且无进展性。检眼镜检查显示有节段性的、灰白色金属光泽，伴有骨针样色素沉着，从视盘沿颞侧血管弓放射，并在黄斑颞侧相连。所有患者的视盘、视网膜血管、周边部和黄斑均正常。视觉功能测试和荧光素血管造影显示为视网膜色素上皮-光感受器复合体的节段性疾病。
