Markowitz J, Daum F, Kahn E I, Schneider K M, So H B, Altman R P, Aiges H W, Alperstein G, Silverberg M
Hepatology. 1983 Jan-Feb;3(1):74-6. doi: 10.1002/hep.1840030112.
Differentiating intrahepatic cholestasis from extrahepatic biliary tract obstruction may be difficult. Four patients with intraoperative cholangiographic evidence of extrahepatic ductal atresia who underwent hepatoportoenterostomy are described. All were ultimately shown to have arteriohepatic dysplasia with hypoplastic but patent extrahepatic ductal systems. The difficulty in establishing an accurate diagnosis, hazards associated with hepatoportoenterostomy, and suggestions for evaluation and management are discussed.
区分肝内胆汁淤积和肝外胆道梗阻可能具有挑战性。本文描述了4例经术中胆管造影证实存在肝外胆管闭锁并接受肝门空肠吻合术的患者。所有患者最终均被证实患有动脉性肝发育不良，其肝外胆管系统发育不全但通畅。文中讨论了准确诊断的困难、肝门空肠吻合术相关的风险以及评估和处理建议。
