Muster A J, Bharati S, Herman J J, Esterly N B, Gonzales-Crussi F, Holbrook K A
J Pediatr. 1983 Feb;102(2):243-8. doi: 10.1016/s0022-3476(83)80529-0.
Acute neutrophilic dermatosis (Sweet syndrome) is a benign self-limited disease in adults. A child with apparent evolution of acute neutrophilic dermatosis to postinflammatory cutis laxa and elastolysis then developed fatal vascular involvement. One other patient with postinflammatory cutis laxa with aortic regurgitation and sudden fatal unrecognized occlusive coronary arterial disease is discussed. If cardiovascular symptoms or signs develop during the course of Sweet syndrome or postinflammatory cutis laxa, a thorough investigation is warranted to rule out potentially fatal coronary arterial disease. Coronary bypass surgery may be the only effective treatment for the severely fibrosed proximal coronary arterial system.
急性嗜中性皮病(Sweet综合征)是一种成人良性自限性疾病。一名儿童急性嗜中性皮病明显演变为炎症后皮肤松弛症和弹性组织离解,随后出现致命的血管受累。还讨论了另一名患有炎症后皮肤松弛症并伴有主动脉瓣反流和突发致命性未被识别的闭塞性冠状动脉疾病的患者。如果在Sweet综合征或炎症后皮肤松弛症病程中出现心血管症状或体征,有必要进行全面检查以排除潜在致命的冠状动脉疾病。冠状动脉搭桥手术可能是严重纤维化的近端冠状动脉系统的唯一有效治疗方法。