先天性肺淋巴管扩张症。1例合并乳糜胸的病例。
Congenital pulmonary lymphangiectasis. A case complicated by chylothorax.
作者信息
Gardner T W, Domm A C, Brock C E, Pruitt A W
出版信息
Clin Pediatr (Phila). 1983 Jan;22(1):75-8. doi: 10.1177/000992288302200112.
PMID:6848293
Abstract
A case is reported of an infant with features of Noonan Syndrome and congenital pulmonary lymphangiectasis. Soon after birth, persistent respiratory distress developed, and, at 4 months of ge, a chylothorax was noted. Medium chain triglyceride therapy by the enteral route was tried, but parenteral alimentation and chest-tube drainage were required. Diagnosis of pulmonary lymphangiectasis was confirmed by biopsy.
摘要
报告了一例患有努南综合征特征及先天性肺淋巴管扩张症的婴儿病例。出生后不久即出现持续性呼吸窘迫，4个月大时发现乳糜胸。尝试了经肠道途径的中链甘油三酯治疗，但仍需要肠外营养和胸腔闭式引流。肺淋巴管扩张症的诊断经活检得以证实。
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