Macfarlane D G, Bourne J T, Dieppe P A, Easty D L
Ann Rheum Dis. 1983 Aug;42(4):398-407. doi: 10.1136/ard.42.4.398.
Classical Wegener's granulomatosis is a relentlessly progressive and rapidly fatal disease. A pulmonary 'limited form' is associated with a much better prognosis. We report 3 cases of Wegener's granulomatosis which ran a prolonged indolent course despite major manifestations outside the lower respiratory tract and review the literature on survival.
典型的韦格纳肉芽肿病是一种持续进展且迅速致命的疾病。肺部“局限型”的预后要好得多。我们报告了3例韦格纳肉芽肿病患者,尽管下呼吸道以外有主要表现,但病程呈长期惰性经过,并复习了有关生存情况的文献。