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儿童期严重脱髓鞘疾病:一项临床病理研究。

Severe demyelinating diseases in childhood: a clinicopathological study.

作者信息

Adams J M

出版信息

J Natl Med Assoc. 1978 Mar;70(3):171-8.

PMID:691079
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2537078/
Abstract

Case reports of six children seen by the author were selected to emphasize that severe demyelinating diseases occur in childhood, even if rarely. Cases include measles encephalitis, acute and chronic, subacute sclerosing panencephalitis, neuromyelitis optica, and multiple sclerosis, confirmed by pathologic findings, and, finally, a case of multiple sclerosis in a living child. Emphasis is directed to the clinical and pathological findings of demyelinating diseases associated with viral encephalitis caused by rubeola and vaccinia viruses. Photomicrographs illustrate the principal pathologic findings.

摘要

作者挑选了六位其所诊治儿童的病例报告,以强调严重的脱髓鞘疾病虽罕见,但也会在儿童期出现。病例包括麻疹脑炎(急性和慢性)、亚急性硬化性全脑炎、视神经脊髓炎和多发性硬化,均经病理检查确诊,最后还有一例在世儿童的多发性硬化病例。重点关注由麻疹病毒和牛痘病毒引起的病毒性脑炎相关脱髓鞘疾病的临床和病理表现。显微照片展示了主要的病理表现。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/67c051f1f558/jnma00013-0031-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/6609c56b65cf/jnma00013-0026-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/2b0a5a0391f6/jnma00013-0027-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/33767cc51a19/jnma00013-0028-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/1c9c17154cc6/jnma00013-0029-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/b6622829526f/jnma00013-0030-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/67c051f1f558/jnma00013-0031-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/6609c56b65cf/jnma00013-0026-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/2b0a5a0391f6/jnma00013-0027-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/33767cc51a19/jnma00013-0028-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/1c9c17154cc6/jnma00013-0029-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/b6622829526f/jnma00013-0030-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c076/2537078/67c051f1f558/jnma00013-0031-a.jpg

相似文献

1
Severe demyelinating diseases in childhood: a clinicopathological study.儿童期严重脱髓鞘疾病:一项临床病理研究。
J Natl Med Assoc. 1978 Mar;70(3):171-8.
2
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4
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5
[Subacute sclerosing panencephalitis].[亚急性硬化性全脑炎]
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Zh Nevropatol Psikhiatr Im S S Korsakova. 1977;77(7):1007-13.
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本文引用的文献

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Neuromyelitis optica: severe demyelination occurring years after primary smallpox vaccination.视神经脊髓炎:原发性天花疫苗接种数年之后发生的严重脱髓鞘病变。
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Isolation of infectious measles virus in measles encephalitis.在麻疹脑炎中分离出感染性麻疹病毒。
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A blood test for multiple sclerosis based on the adherence of lymphocytes to measles-infected cells.一种基于淋巴细胞与麻疹感染细胞黏附情况的多发性硬化症血液检测方法。
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Immunoglobulin abnormalities and measles antibody response in chronic myelopathy.
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