Adams J M
J Natl Med Assoc. 1978 Mar;70(3):171-8.
Case reports of six children seen by the author were selected to emphasize that severe demyelinating diseases occur in childhood, even if rarely. Cases include measles encephalitis, acute and chronic, subacute sclerosing panencephalitis, neuromyelitis optica, and multiple sclerosis, confirmed by pathologic findings, and, finally, a case of multiple sclerosis in a living child. Emphasis is directed to the clinical and pathological findings of demyelinating diseases associated with viral encephalitis caused by rubeola and vaccinia viruses. Photomicrographs illustrate the principal pathologic findings.
作者挑选了六位其所诊治儿童的病例报告,以强调严重的脱髓鞘疾病虽罕见,但也会在儿童期出现。病例包括麻疹脑炎(急性和慢性)、亚急性硬化性全脑炎、视神经脊髓炎和多发性硬化,均经病理检查确诊,最后还有一例在世儿童的多发性硬化病例。重点关注由麻疹病毒和牛痘病毒引起的病毒性脑炎相关脱髓鞘疾病的临床和病理表现。显微照片展示了主要的病理表现。