Olbert F, Kobinia G, Russe O J, Denck H
Wien Med Wochenschr Suppl. 1980;65:1-26.
An aneurysm of the vena azygos should be taken into consideration when establishing the differential diagnosis of a tumor in the area of the right tracheobronchial angle or of an enlargement of the right upper mediastinum. Bilateral pelvic phlebography with demonstration of the retroperitoneal venous system and the azygos venous system is the only purposeful examination. Tentative diagnosis is made on the basis of the X-ray (radioscopy and general X-ray of the chest) and is supplemented by X-rays of the patient in a recumbent position (Valsalva- and Müller-test) and appropriate tomography. The most frequent cause of the azygos aneurysm in our patients was aplasia of the inferior vena cava. One patient presented an infrahepatic interruption of the inferior vena cava with azygos continuation. Phlebography of the inferior vena cava should always be performed in cases of azygos aneurysm. An abnormality of the inferior vena cava may be missing; in such cases the existence of a cardiac defect, abnormal emptying of pulmonary veins or hepatic cirrhosis should be taken into consideration. The enlargement of the azygotic arch may also occur during pregnancy. Thus an azygos aneurysm is frequently but not necessarily associated with enlargement of the azygotic arch. We saw one patient among our cases who presented aplasia of the inferior vena cava without any dilatation of the azygotic arch.
在对右气管支气管角区域的肿瘤或右上纵隔增宽进行鉴别诊断时,应考虑奇静脉瘤。双侧盆腔静脉造影以显示腹膜后静脉系统和奇静脉系统是唯一有针对性的检查。初步诊断基于X线检查(荧光透视和胸部普通X线片),并辅以患者卧位时的X线检查(瓦尔萨尔瓦试验和米勒试验)及适当的体层摄影。在我们的患者中,奇静脉瘤最常见的原因是下腔静脉发育不全。1例患者表现为下腔静脉肝下中断伴奇静脉延续。对于奇静脉瘤病例,应始终进行下腔静脉静脉造影。下腔静脉异常可能不明显;在这种情况下,应考虑存在心脏缺陷、肺静脉排空异常或肝硬化。奇静脉弓增宽也可能在妊娠期间出现。因此,奇静脉瘤常与奇静脉弓增宽相关,但并非必然如此。我们在病例中看到1例患者,其下腔静脉发育不全,但奇静脉弓无任何扩张。