Gussen R
Ann Otol Rhinol Laryngol. 1980 Mar-Apr;89(2 Pt 1):157-61. doi: 10.1177/000348948008900212.
Unilateral endolymphatic hydrops is described associated with absence of the vein in the paravestibular canaliculus (PVC), and with decreased vascularity of the vestibular aqueduct and endolymphatic sac. The venous return from the vestibule was normal as far as the junction of the branches forming the PVC vein. At this junction, a blind venous loop was formed with no continuation of venous drainage through the PVC. This probably represents a developmental anomaly. The decreased vascularity of the endolymphatic sac may be related to the absence of the PVC vein. However, anatomical and functional relationships of these vessels are not clear and need further study. Perisac fibrosis and endosteal bone formation are possibly secondary to the decrease in vascularity. A large chronic rupture of the inferior saccule wall probably accounts for the absence of vertigo and the relatively mild degree of cochlear endolymphatic hydrops.
单侧内淋巴积水被描述为与前庭旁小管（PVC）内静脉缺如、前庭导水管和内淋巴囊血管减少有关。从前庭的静脉回流直至形成PVC静脉的分支交汇处均正常。在这个交汇处，形成了一个盲端静脉环，没有静脉引流通过PVC延续。这可能代表一种发育异常。内淋巴囊血管减少可能与PVC静脉缺如有关。然而，这些血管的解剖和功能关系尚不清楚，需要进一步研究。囊周纤维化和骨内膜骨形成可能继发于血管减少。下椭圆囊壁的大的慢性破裂可能是眩晕缺如和耳蜗内淋巴积水程度相对较轻的原因。
