Schwöbel M G, Uhlschmid G
Schweiz Med Wochenschr. 1982 Apr 17;112(16):571-5.
The case of a 22-year-old patient with a thoracoabdominal duplication of the alimentary tract is described. The chest radiograph, with a large cyst in the posterior mediastinum and vertebral abnormalities and a barium swallow showing the abdominal part of the duplication, were diagnostic. At operation a malrotation of the midgut was found and the duplication was resected, leaving esophagus and small bowel intact. An explanation for association of the two malformations - vertebral abnormalities and malrotation - was sought in the literature, particularly that concerning embryogenesis. The following conclusions were reached: 1. Duplications of the alimentary tract are a heterogeneous group with three different embryological faults in development. 2. According to the so-called notochordal theory, vertebral abnormalities and malrotation of the midgut are usual and should be expected in thoracoabdominal duplications of the alimentary tract.
本文描述了一名22岁患有胸腹部消化道重复畸形患者的病例。胸部X光片显示后纵隔有一个大囊肿且伴有椎体异常,吞钡检查显示了重复畸形的腹部部分,这些检查具有诊断意义。手术中发现中肠旋转不良,切除了重复畸形部分,食管和小肠保持完整。在文献中,特别是关于胚胎发生学的文献中,寻找了两种畸形(椎体异常和旋转不良)关联的解释。得出以下结论:1. 消化道重复畸形是一组异质性疾病,在发育过程中有三种不同的胚胎学缺陷。2. 根据所谓的脊索理论,椎体异常和中肠旋转不良在胸腹部消化道重复畸形中很常见,应该预料到。