Moreira Filho P F, Freitas M R, Hahn M D, Cincinatus D, Nascimento O J
Arq Neuropsiquiatr. 1982 Jun;40(2):146-55. doi: 10.1590/s0004-282x1982000200004.
Two cases of Lance-Adams syndrome with anatomopathologic study are reported. There were evidences of diffuse neuronal degeneration in the brain. These changes were most seen in the neurones of the cortical layers, thalamus and subthalamic nuclei. The cells changes were similar to those seen in ischaemic disease. Some neurones showed intracytoplasmatic inclusions staining with the P.A.S. method. These inclusions were readily distinguished from the Lafora bodies.
报告了两例伴有解剖病理学研究的兰斯-亚当斯综合征病例。脑内有弥漫性神经元变性的证据。这些变化在皮质层、丘脑和丘脑底核的神经元中最为明显。细胞变化与缺血性疾病中所见的相似。一些神经元显示出经P.A.S.法染色的胞质内包涵体。这些包涵体很容易与拉福拉小体区分开来。
