Wittich G, Czembirek H, Fridrich L, Imhof H
Radiologe. 1980 Nov;20(11):534-9.
The efficiency of radiological methods in the diagnosis of visceral manifestations of Hippel-Lindau Syndrome is discussed by means of a case report as well as by the results from studies of other authors. The importance of detecting small renal malignancies (often occurring bilaterally and multifocally in this disease) is stressed since benign (cystic, adenomatous, angiomatous) lesions of visceral organs are of minor clinical relevance. Pheochromocytomas, found in about 20% of cases, are primarily diagnosed clinically. The diagnostic goal of precise quantification of neoplastic renal tumors and of unequivocal differentiation between cystic and solid lesions appears to be achieved by the combination of computertomographic and pharmaco-angiographic techniques. A prerequisite for the alternative use of ultrasound is optimal imaging of all parts of renal parenchyma.
通过一份病例报告以及其他作者的研究结果,探讨了放射学方法在诊断希佩尔-林道综合征内脏表现中的效率。强调了检测小的肾恶性肿瘤(在该疾病中常双侧多发)的重要性,因为内脏器官的良性(囊性、腺瘤性、血管瘤性)病变临床意义较小。约20%的病例中发现的嗜铬细胞瘤主要通过临床诊断。计算机断层扫描和药物血管造影技术相结合似乎实现了精确量化肿瘤性肾肿瘤以及明确区分囊性和实性病变的诊断目标。超声替代使用的一个前提是肾实质所有部分的最佳成像。