Magri G, Puccetti U, Cremonesi G, Sardella F, Avanzi C
G Ital Cardiol. 1981;11(1):132-8.
In progressive systemic sclerosis, cardiac involvement, evidenced by histology, is rather unusual and even more rarely it gives clinical manifestations. In our patient cardiac symptoms, characterized by recurrent pulmonary edema as well as by serious conduction defects and arrhythmias, are prevailing and have a rapid and fatal course, whereas the involvement of the skin and of other internal organs is not important. The post-mortem examination gives an evident explanation of the clinical course of the disease, which we can consider as a typical manifestation of sclerodermic heart.
在进行性系统性硬化症中，经组织学证实的心脏受累相当罕见，更罕见的是出现临床表现。在我们的患者中，以反复出现肺水肿、严重传导缺陷和心律失常为特征的心脏症状占主导，且病程迅速且致命，而皮肤和其他内脏器官的受累并不严重。尸检对该疾病的临床病程给出了明确解释，我们可将其视为硬皮病性心脏病的典型表现。
