Martinenghi P, Broggi A, Paganini E, Battaglia A, Marelli A, Dozio F, Bisazza R, Ermolli M
Chir Ital. 1980 Oct;32(5):1248-53.
The clinical case of a sixty-two year old woman suffering for about six years from rare episodes of cramplike pains in the right hypochondriac region, radiated to the homolateral scapula, is described. After diagnosis of biliary calculosis, the patient was admitted to hospital and her gallbladder removed. During the operation a number of venous ectasias of the portal system were evidenced at the hepatic hilus, and their biopsy led to a diagnosis of portal cavernoma. The possible part played by the cavernoma in producing the patient's clinical picture is discussed, with reference also to other cases of cavernoma of varying location. This is followed by a review of the literature, in which stress is placed on the different aetiopathogenetic interpretations of angiomas and in particular of portal cavernomas. The possible evolution of angiomas and present treatment trends are also mentioned.
本文描述了一位62岁女性的临床病例，她右侧季肋区出现类似抽筋样疼痛的罕见发作症状约六年，疼痛放射至同侧肩胛骨。在诊断为胆石症后，患者入院并接受了胆囊切除术。手术过程中，在肝门处发现了门静脉系统的一些静脉扩张，对其进行活检后诊断为门静脉海绵样变性。文中讨论了海绵样变性在导致患者临床表现中可能起到的作用，并参考了其他不同部位海绵样变性的病例。随后对文献进行了综述，着重介绍了血管瘤尤其是门静脉海绵样变性的不同病因学解释。还提及了血管瘤可能的发展过程及目前的治疗趋势。
