Slim M S, Pimpalnerkar L, Rao S S, Ali A H, Hajar H A
Z Kinderchir. 1981 Sep;34(1):67-71. doi: 10.1055/s-2008-1063299.
A 12-year-old girl with a solitary pulmonary arterio-venous fistula (P.A.V.F.) affecting the R.L.L. is reported. The cyanosis was noted since birth and increased with age. The diagnosis was confirmed by right heart catheterization and pulmonary arteriography. Preoperatively, her hematocrit was 73%, paO2 36 mm Hg and no bruit was heard. The treatment consisted of a right lower lobectomy. One year postoperatively, the patient has normal activities, is asymptomatic and has no evidence of residual disease. A short review of the literature on the subject of P.A.V.F. is included and indicates the relative rarity of surgical treatment of this disease in childhood.
报告了一名12岁女孩，患有影响右下叶的孤立性肺动静脉瘘（P.A.V.F.）。自出生起即发现有紫绀，并随年龄增长而加重。通过右心导管检查和肺动脉造影确诊。术前，她的血细胞比容为73%，动脉血氧分压为36毫米汞柱，未闻及杂音。治疗方法为右下叶切除术。术后一年，患者活动正常，无症状，且无残留疾病迹象。文中还对有关P.A.V.F.这一主题的文献进行了简短回顾，表明该疾病在儿童期进行手术治疗相对罕见。
