Hayakawa H, Iwata T, Yata J, Kobayashi N
J Clin Immunol. 1981 Jan;1(1):31-9. doi: 10.1007/BF00915474.
The results of a nationwide survey on primary immunodeficiency syndrome (PIS) in Japan are presented. By the repeated questionnaire method, 497 PIS cases were collected prior to February 1979 with clinical information. Numbers of each type of PIS, age at the time of diagnosis, patient's status at the time of registration, familial incidence of PIS, and development of malignancy, autoimmune diseases, and allergic diseases among all reported patients are presented and discussed.
本文展示了一项关于日本原发性免疫缺陷综合征（PIS）的全国性调查结果。通过重复问卷调查法，在1979年2月之前收集了497例PIS病例及其临床信息。文中呈现并讨论了各类PIS的数量、诊断时的年龄、登记时患者的状况、PIS的家族发病率，以及所有报告患者中恶性肿瘤、自身免疫性疾病和过敏性疾病的发生情况。
