Schipperheyn J J, Buruma O J, Voogd P J
Acta Neurol Scand. 1978 Dec;58(6):374-8. doi: 10.1111/j.1600-0404.1978.tb02902.x.
The results are reported of cardiological examinations, including echocardiography, in nine members of a family suffering from hypokalaemic periodic paralysis, associated with permanent muscular weakness. The studies were performed in periods between attacks of paralysis. The slowly progressive permanent muscular weakness which is found in most of the patients with hypokalaemic periodic paralysis resembles a limb-girdle type dystrophy. Involvement of cardiac muscle is not uncommon in patients with limb-girdle dystrophy. Using a combination of echocardiography and ECG examination, nowadays the most sensitive screening method for the detection of cardiomyopathy, no evidence was obtained for cardiac involvement in hypokalaemic periodic paralysis patients with permanent muscular weakness.
本文报告了对一个患有低钾性周期性麻痹并伴有永久性肌肉无力的家族中九名成员进行的心脏病学检查结果，包括超声心动图检查。这些研究是在麻痹发作间歇期进行的。在大多数低钾性周期性麻痹患者中发现的缓慢进展的永久性肌肉无力类似于肢带型肌营养不良。在肢带型肌营养不良患者中，心肌受累并不罕见。如今，超声心动图和心电图检查相结合是检测心肌病最敏感的筛查方法，但在患有永久性肌肉无力的低钾性周期性麻痹患者中，未获得心脏受累的证据。
