低钾性周期性麻痹发作期间的表面肌电图和肌纤维传导
Surface EMG and muscle fibre conduction during attacks of hypokalaemic periodic paralysis.
作者信息
Links T P, van der Hoeven J H, Zwarts M J
机构信息
Department of Internal Medicine, University Hospital, Groningen, The Netherlands.
出版信息
J Neurol Neurosurg Psychiatry. 1994 May;57(5):632-4. doi: 10.1136/jnnp.57.5.632.
Abstract
Surface EMG, muscle fibre conduction velocity (MFCV), muscle force, and biochemical variables were investigated in a 13-year-old boy with familial hypokalaemic periodic paralysis during and after three attacks of paralysis. After normalisation of the serum potassium values, strength rapidly returned to interictal values, but the integrated EMG and to a lesser extent the MFCV recovered more slowly. These findings suggest that a complete electrophysiological recovery is not necessary for a restoration of muscle force and that the pathogenetic defect is localised in the muscle membrane.
摘要
在一名患有家族性低钾性周期性麻痹的13岁男孩的三次麻痹发作期间及之后，对其表面肌电图、肌纤维传导速度（MFCV）、肌力和生化变量进行了研究。血清钾值恢复正常后，肌力迅速恢复到发作间期水平，但积分肌电图以及程度较轻的MFCV恢复得更慢。这些发现表明，肌力恢复并不一定需要完全的电生理恢复，并且致病缺陷定位于肌膜。
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