Schinzel A, Schmid W
Am J Med Genet. 1980;6(3):241-9. doi: 10.1002/ajmg.1320060308.
Two unrelated patients, a 4-year-old boy and a 2 1/2-year-old girl, presented with a similar pattern of abnormalities. Both had severe mental retardation, macrocephaly, absence of the corpus callosum, unusual facial appearance, duplication of hallucal phalanges, postaxial hexadactyly of finger phalanges, and 2/3-syndactyly of toes. The boy also had postaxial hexadactyly of toe phalanges, inguinal hernias and umbilical hernia, and growth retardation. We suspect a common cause of this apparently "new" syndrome, most likely a gene mutation.
两名无血缘关系的患者,一名4岁男孩和一名2岁半女孩,表现出相似的异常模式。两人均有严重智力发育迟缓、巨头畸形、胼胝体缺失、特殊面容、拇趾指骨重复、手指远轴多指畸形以及2/3足趾并指畸形。该男孩还患有足趾远轴多指畸形、腹股沟疝和脐疝以及生长发育迟缓。我们怀疑这种明显的“新”综合征有一个共同病因,很可能是基因突变。