Antico L, Coppola E, Schiavoni G, Spadaccia P L, Compagnoni A, Cocco F
G Ital Cardiol. 1980;10(9):1212-8.
The scimitar syndrome groups a combination of several congenital anomalies in the right lung with an abnormal right pulmonary venous drainage in the inferior vena cava or the right atrium. After a survey of 130 cases in the literature, clinical, angiografic and hemodynimac features of the syndrome are defined. The Authors report two new cases diagnosed in adults, characterised by a clean discordance between the clinical features and the angiographic ones. The former case is completely asymptomatic and the radiographic feature is typical, while the latter shows a characteristic symptomatology but there isn't a clean "scimitar image". But notwithstanding the absence of this "scimitar image", the Authors think that the anomalous pulmonary drainage in the right atrium and the several anomalies in the right lung can be attributed to the scimitar syndrome, physiopatologically.
弯刀综合征是指右肺的几种先天性异常与下腔静脉或右心房异常的右肺静脉引流相结合。在对文献中的130例病例进行研究后，明确了该综合征的临床、血管造影和血流动力学特征。作者报告了两例在成人中诊断出的新病例，其临床特征与血管造影特征明显不一致。前一例完全无症状，影像学特征典型，而后一例表现出典型症状，但没有清晰的“弯刀影像”。但尽管没有这种“弯刀影像”，作者认为右心房的异常肺静脉引流和右肺的几种异常在病理生理学上可归因于弯刀综合征。
