Esteban I, Cabrera A, Azcuna J I, Cuadrado P V
An Esp Pediatr. 1977 Jun-Jul;10(6-7):543-56.
Four cases between one day of life and seven years are presented. Two of them were males and two females. All of them had cardiac pulsation palpable to the right of the sternum, one with some bulging of the left hemitorax. In two cases a systolic murmur was heard over the second intercostal space associated with fixed splitting of the second sound and the other case presented recurrent infections processes of the lung dying ultimately from bronchoneumonia. On the simple X-ray displacement of the mediastine towards the right side, dextroposition of the heart, right pulmonary hyoplasia, enlargement of the right atrium and image in "scimitar" (obvious in two cases and possibly existed in the other two) was observed. In three cases a lung scan was carried out which showed a marked decrease in perfusion of the right lung. Angiocardiography in all cases as able to demonstrate anomalous venous drainage of the right lung to inferior vena cava directly.
本文报告了4例年龄在出生1天至7岁之间的病例。其中2例为男性，2例为女性。所有病例均在胸骨右侧可触及心脏搏动，1例伴有左侧胸廓轻度隆起。2例在第二肋间可闻及收缩期杂音，伴有第二心音固定分裂，另1例反复发生肺部感染，最终死于支气管肺炎。单纯X线检查可见纵隔向右移位、心脏右位、右肺发育不全、右心房增大以及“弯刀征”影像（2例明显，另2例可能存在）。3例行肺扫描，显示右肺灌注明显减少。所有病例的心血管造影均显示右肺静脉直接异常引流至下腔静脉。
