Deramond H, Remond A, Grumbach Y, Dieval M, Coevoet B, Duriez J, Katz M
J Radiol. 1980 Aug-Sep;61(8-9):503-8.
Bone radiological signs in six cases of systemic mastocytosis are described: lesions may be diffuse or circumscribed and of the condensation and/or rarefaction type. In most cases, however, the lesions are of the mixed type. Bone mastocytosis may occur without any cutaneous lesions and this emphasizes the value, from the diagnostic point of view, of radiological examinations of the skeleton. Diagnosis is defined and confirmed by three features: the association of condensing lesions and bone rarefactions in different regions of the skeleton; the presence of mastocytic proliferation in stained biopsy specimens from the posterior iliac bone which is not decalcified; fixation of 99m tc pyrophosphate in the axial skeleton on scintigraphy.
本文描述了6例系统性肥大细胞增多症的骨骼放射学征象：病变可为弥漫性或局限性，呈骨质致密和/或骨质稀疏型。然而，在大多数情况下，病变为混合型。骨肥大细胞增多症可能在没有任何皮肤病变的情况下发生，这从诊断角度强调了骨骼放射学检查的价值。诊断通过以下三个特征来定义和确认：骨骼不同区域存在致密性病变和骨质稀疏；来自未脱钙的髂后骨的染色活检标本中存在肥大细胞增殖；骨闪烁显像显示99m锝焦磷酸盐在中轴骨骼的摄取。
