Harada K, Seki I, Kobayashi H, Okuni M, Sakurai I
Jpn Heart J. 1980 Nov;21(6):903-10. doi: 10.1536/ihj.21.903.
A 7-year-old boy presented with intermittent systolic murmur and syncope. Chest roentgenogram revealed mild cardiomegaly. Electrocardiogram showed right bundle branch block and abnormal T-waves. Right ventricular angiography demonstrated a filling defect at the anterior portion of the right ventricular cavity and histological examination of biopsy specimen revealed lipoma. At operation, the tumor could not be totally resected. Histological examination of surgical specimen showed marked proliferation of mature fat cells between cardiac muscle fibers. Postoperatively he has been remained asymptomatic. Postoperative standard M-mode and two-dimensional echocardiogram demonstrated a mass from right ventricular wall, abnormal motion of the interventricular septum and small left atrial cavity. The patient has been followed by serial echocardiography.
一名7岁男孩出现间歇性收缩期杂音和晕厥。胸部X线片显示轻度心脏扩大。心电图显示右束支传导阻滞和T波异常。右心室血管造影显示右心室腔前部有充盈缺损,活检标本的组织学检查显示为脂肪瘤。手术时,肿瘤无法完全切除。手术标本的组织学检查显示心肌纤维间成熟脂肪细胞显著增生。术后他一直无症状。术后标准M型和二维超声心动图显示右心室壁有肿块、室间隔运动异常和左心房小腔。该患者接受了系列超声心动图随访。