Rudolph R I
Cutis. 1981;27(1):82-4.
Lung involvement in tuberous sclerosis is rare. Those patients with lung involvement differ from the usual tuberous sclerosis patient in that they are predominantly women, are of normal intelligence, and are less likely to develop epilepsy. The lung disease is often fatal, with cor pulmonale and pneumothorax as the major causes of death. A review of the radiologic and pathophysiologic findings of the lung process are also presented in the following case report.
结节性硬化症累及肺部的情况较为罕见。那些肺部受累的患者与普通结节性硬化症患者不同，他们以女性为主，智力正常，且患癫痫的可能性较小。肺部疾病往往是致命的，肺心病和气胸是主要死因。以下病例报告还对肺部病变的放射学和病理生理学发现进行了综述。
