Lelli S, Trevisan C, Negrin P
Servizio di EMG e Neurofisiologia Clinica, Università di Padova, Italy.
Electromyogr Clin Neurophysiol. 1995 Aug-Sep;35(5):311-5.
Eight patients affected by Ataxia-Teleangectasia (AT) were studied with a set of neurophysiological tests. The study was done two times between 2 and 10 years. The most characteristic feature was a severe involvement of the posterior spinal cord: it was associated with a moderate peripheral neuropathy as well as a severe peripheral neuropathy. These data could indicate that the dying back phenomena are not the only pathogenetic basis of the spinal cord degeneration in this disease.
对8例患有共济失调毛细血管扩张症（AT）的患者进行了一系列神经生理学测试。该研究在2至10年期间进行了两次。最典型的特征是脊髓后索严重受累：它与中度周围神经病变以及重度周围神经病变相关。这些数据表明，轴突逆行性变性现象并非该疾病脊髓变性的唯一发病机制基础。
