婴儿遗传性粒细胞缺乏症（科斯特曼型）。病例报告。
Infantile genetic agranulocytosis (Kostmann type). A case report.
作者信息
Sağlam F, Atamer T, Onan U, Soydinç M, Kiraç K
机构信息
University of Istanbul, Faculty of Dentistry, Department of Periodontology, Turkey.
出版信息
J Periodontol. 1995 Sep;66(9):808-10. doi: 10.1902/jop.1995.66.9.808.
Severe periodontitis in a patient with infantile genetic agranulocytosis (Kostmann syndrome) is presented. This rare syndrome is inherited as an autosomal recessive pattern and characterized by severe neutropenia. The periodontal status and treatment of the patient is described. It is concluded that periodontal therapy including scaling, root planning, soft tissue curettage, and the use of selected antimicrobial agents can be successful in this particular syndrome.
本文介绍了一名患有婴儿遗传性粒细胞缺乏症（科斯特曼综合征）患者的重度牙周炎。这种罕见的综合征以常染色体隐性模式遗传，其特征为严重的中性粒细胞减少症。文中描述了该患者的牙周状况及治疗情况。得出的结论是，包括龈上洁治、根面平整、软组织刮治以及使用特定抗菌药物在内的牙周治疗，对于这一特殊综合征可能会取得成功。
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