Fourcade L, van de Walle J P, Nicolas X, Deharo J C, Djiane P, Touze J E
Service de Cardiologie, HIA Laveran, Marseille Armees.
Ann Cardiol Angeiol (Paris). 1995 Mar;44(3):125-30.
Arrhythmogenic right ventricular dysplasia is one of the principal causes of sudden cardiac death in young subjects. In the absence of ventricular tachycardia, the disease can be revealed by simple ventricular extrasystole. In the light of such a case, the authors discuss the value of various complementary investigations for the diagnosis of these clinical forms with little or no symptoms. Detailed examination of the electrocardiogram followed by a search for late ventricular potentials are decisive steps before proceeding to invasive investigations which often remain essential to confirm the diagnosis. The prognosis remains uncertain, and is always dominated by the risk of sudden death, even in these apparently minor forms of the disease. This point further emphasizes the need for detection, which should be facilitated by the recent establishment of a list of diagnostic criteria.
致心律失常性右心室发育不良是年轻人群心脏性猝死的主要原因之一。在无室性心动过速的情况下，该病可通过单纯室性期前收缩得以发现。鉴于这样一个病例，作者讨论了各种辅助检查对于诊断这些轻微或无症状临床类型的价值。在进行往往对确诊仍至关重要的侵入性检查之前，详细检查心电图并随后查找晚期心室电位是决定性步骤。预后仍然不确定，并且始终以猝死风险为主导，即使在这些看似轻微的疾病形式中也是如此。这一点进一步强调了检测的必要性，而最近制定的诊断标准清单应有助于检测工作。
