Nakanishi H, Hashimoto I, Takiwaki H, Urano Y, Arase S
Department of Dermatology, School of Medicine, University of Tokushima, Japan.
J Dermatol. 1995 Jul;22(7):504-7. doi: 10.1111/j.1346-8138.1995.tb03433.x.
We observed two females, an 11-month old and a 15-year-old, each with a round, soft mass in the nostril. Histologically, numerous bundles of striated muscle fibers were seen in the masses among normal dermal components. The lesions were excised without complications. Four patients with similar lesions confirmed clinically and histologically have been reported in the literature under various diagnostic names. These masses were diagnosed as striated muscle hamartomas in view of their characteristic features: congenital round, soft masses on the midline of the head or neck with multiple, mature striated muscles observed in the mass. Since these lesions may be associated with such anomalies as amniotic band syndrome and lipoma of the brain, a complete medical examination is required of such patients.
我们观察到两名女性患者，一名11个月大，另一名15岁，她们的鼻孔内均有一个圆形的柔软肿物。组织学检查显示，在肿物中可见众多横纹肌纤维束，其间夹杂着正常的皮肤成分。病变被切除，未出现并发症。文献中曾报道过另外4例经临床和组织学确诊的类似病变患者，诊断名称各异。鉴于这些肿物的特征：头部或颈部中线处先天性圆形柔软肿物，肿物内可见多个成熟的横纹肌，故将其诊断为横纹肌错构瘤。由于这些病变可能与羊膜带综合征和脑脂肪瘤等异常情况相关，因此需要对这类患者进行全面的医学检查。
