Geromino A, Verduci G, Paoni A, Elmi F, Bottaru M, Bercovich E
Istituto di Clinica Urologica, Università di Sassari.
Arch Ital Urol Androl. 1995 Sep;67(4):261-3.
Angiomyolipoma is a rare tumor frequently associated with tuberous sclerosis and it has a higher incidence of bilateral renal involvement in this case. Patients effected by Bourneville's Syndrome are often more symptomatic than patients with angiomyolipoma only, however it is necessary to examine the renal conditions in all of them because of the high risk for severe hemorrhage. Diagnostic evaluation is based on radiological findings as Ultrasonography and Computed Tomography. We present a case of bilateral and symptomatic angiomyolipoma is a young woman with Bourneville's Syndrome.
血管平滑肌脂肪瘤是一种罕见肿瘤，常与结节性硬化症相关，在这种情况下双侧肾受累的发生率更高。患有结节性硬化症的患者通常比仅患有血管平滑肌脂肪瘤的患者症状更明显，然而，由于严重出血的高风险，对所有患者进行肾脏状况检查是必要的。诊断评估基于超声和计算机断层扫描等影像学检查结果。我们报告一例患有结节性硬化症的年轻女性双侧有症状血管平滑肌脂肪瘤的病例。
