Sola J E, Pierre-Jerome F, Sitzmann J V, Wheeler J, Bizzi A, Terotola S O
Department of Surgical Oncology, Johns Hopkins Medical Institutions, Baltimore, Maryland, USA.
Clin Imaging. 1996 Apr-Jun;20(2):99-102. doi: 10.1016/0899-7071(94)00080-8.
Angiomyolipomas are rare lesions that occur most commonly in the kidney, but also can occur in the liver and rarely, in the lymph nodes. Its rare association with tuberous sclerosis has been suggested, but never proved. We report a patient with multiple visceral angiomyolipomas as well as visceral vessel aneurysms and tuberous sclerosis. The association of the three lesions suggests a possible common connective-tissue defect.
血管平滑肌脂肪瘤是一种罕见的病变，最常发生于肾脏，但也可发生于肝脏，极少发生于淋巴结。曾有人提出它与结节性硬化症存在罕见关联，但从未得到证实。我们报告一例患有多发性内脏血管平滑肌脂肪瘤、内脏血管动脉瘤及结节性硬化症的患者。这三种病变的关联提示可能存在一种共同的结缔组织缺陷。
