Kawahira Y, Kishimoto H, Lio M, Ikawa S, Kume Y, Inamura N, Matushita T, Maeno T, Nakada T
Department of Cardiovascular Surgery, Osaka Medical Center, Japan.
Cardiovasc Surg. 1995 Apr;3(2):219-21. doi: 10.1016/0967-2109(95)90899-g.
Spontaneous aortic thrombosis in the neonate is a rare entity with a high mortality rate. The present patient, who was diagnosed after showing haematuria and cyanosis, underwent aortic thrombectomy with a Fogarty catheter through a left thoracotomy, but died of sepsis, disseminated intravascular coagulation and multiple organ failure. Autopsy revealed multiple residual thrombi in the main branches of the abdominal aorta and necrosis of the abdominal organs despite a patent thoracoabdominal aorta. In patients with no blood flow in the main branches of the abdominal aorta on preoperative examination, removal of thrombi, including those in the main branches of the abdominal aorta, might be performed in a single, early and aggressive procedure.
新生儿自发性主动脉血栓形成是一种罕见的疾病,死亡率很高。本例患者在出现血尿和发绀后被诊断出来,通过左胸切开术用Fogarty导管进行了主动脉血栓切除术,但死于败血症、弥散性血管内凝血和多器官功能衰竭。尸检发现,尽管胸腹主动脉通畅,但腹主动脉主要分支中有多个残留血栓,腹部器官有坏死。对于术前检查发现腹主动脉主要分支无血流的患者,可能需要在单一、早期且积极的手术中清除包括腹主动脉主要分支内的血栓。