Sessa A, Pietrucci A, Carozzi S, Torri Tarelli L, Tazzari S, Giordano F, Meroni M, Battini G, Valente U, Renieri A
UO Nefrologia e Dialisi, Ospedale, Vimercate, Italy.
Nephron. 1995;70(1):106-9. doi: 10.1159/000188553.
Renal transplantation from living donor parents was performed in two brothers with end-stage renal failure due to Alport syndrome (AS). Two years later, the patient receiving the kidney graft from the mother, obligate carrier of AS, presented persistent microhematuria and proteinuria with normal renal function. The histological study demonstrated ultrastructural glomerular lesions consistent with AS. The authors conclude that: (1) Alport patients should not be deprived of renal transplantation from living donors, since anti-GBM nephritis is a rare complication; (2) an oligosymptomatic female carrier of the Alport gene may be considered as living renal donor, although a longer follow-up is needed in order to draw definitive conclusions.
对两名因奥尔波特综合征(AS)导致终末期肾衰竭的兄弟进行了来自活体供体父母的肾移植。两年后,接受来自AS携带者母亲肾脏移植的患者,肾功能正常,但出现持续性镜下血尿和蛋白尿。组织学研究显示肾小球超微结构病变与AS相符。作者得出结论:(1)不应剥夺AS患者接受活体供体肾移植的机会,因为抗肾小球基底膜肾炎是一种罕见的并发症;(2)尽管需要更长时间的随访才能得出明确结论,但奥尔波特基因的无症状女性携带者可被视为活体肾供体。