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新生儿因腱索断裂继发严重三尖瓣反流,酷似三尖瓣上的肿块。

Critical tricuspid regurgitation secondary to ruptured chordae tendineae mimicking a mass on the tricuspid valve in a newborn.

作者信息

Atalay S, Imamoglu A, Uluoglu O, Ikizler C

机构信息

Department of Pediatric Cardiology, Ankara University, Turkey.

出版信息

Pediatr Cardiol. 1995 May-Jun;16(3):133-6. doi: 10.1007/BF00801912.

Abstract

Tricuspid regurgitation (TR) due to chordal rupture is a rare condition in newborns. We present a newborn with critical TR. Cross-sectional echocardiography demonstrated a dense, mobile mass localized at the tricuspid valve and resembling an atrial thrombus or myxoma. At operation, ruptured chordae tendineae of the tricuspid valve were found, forming a tangled mass. Histopathologic examination revealed collagen degeneration and calcification in the ruptured chordae, producing the hyperechoic image. It should be emphasized that ruptured chordae of the tricuspid valve might mimic a tricuspid valve myxoma or a thrombus on cross-sectional echocardiography.

摘要

因腱索断裂导致的三尖瓣反流(TR)在新生儿中是一种罕见病症。我们报告一例患有严重TR的新生儿。横断面超声心动图显示一个致密的、可移动的肿块位于三尖瓣处,类似心房血栓或黏液瘤。手术时发现三尖瓣腱索断裂,形成一团纠结物。组织病理学检查显示断裂腱索中有胶原变性和钙化,产生了高回声图像。应当强调的是,三尖瓣腱索断裂在横断面超声心动图上可能会被误诊为三尖瓣黏液瘤或血栓。

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