Marquart H V, Svendsen A, Rasmussen J M, Nielsen C H, Junker P, Svehag S E, Leslie R G
Department of Medical Microbiology, Odense University, Denmark.
Clin Exp Immunol. 1995 Jul;101(1):60-5. doi: 10.1111/j.1365-2249.1995.tb02277.x.
It has previously been reported that the expression of the complement receptors, CR1 on erythrocytes and blood leucocytes and CR2 on B cells, is reduced in patients with SLE, and that the reduced expression of CR1 on erythrocytes is related to disease activity. We have earlier demonstrated that normal B cells are capable of activating the alternative pathway (AP) of complement in a CR2-dependent fashion. In this study we have investigated whether disturbances in this activity may be related to the altered phenotype of SLE B cells. Flow cytometry was used to measure expression of complement receptors and regulatory proteins on B cells from SLE patients, as well as the deposition of C3 fragments occurring in vivo or after in vitro AP activation. We have confirmed, for a proportion of the patients studied, reduced expression of CR1 and CR2 on B cells, and shown a consistency between low CR2 expression and reduced in vitro AP activation in the presence of homologous, normal serum. In addition, the B cells, like erythrocytes, bear raised levels of in vivo-deposited C3dg, but not C3b fragments, compared with normal B cells. The erythrocytes from SLE patients were unable to inhibit in vitro AP activation by B cells in homologous serum. Finally, we demonstrated an inverse relationship between SLE disease activity index (SLEDAI) and the expression of complement receptor 2 (CR2) on SLE B cells. Thus, determination of CR2 on B cells may emerge as an additional laboratory tool in the assessment of SLE activity.
此前有报道称,系统性红斑狼疮(SLE)患者红细胞和血液白细胞上的补体受体CR1以及B细胞上的CR2表达降低,且红细胞上CR1表达降低与疾病活动度相关。我们之前已证明,正常B细胞能够以CR2依赖的方式激活补体替代途径(AP)。在本研究中,我们调查了这种活性的紊乱是否可能与SLE B细胞的表型改变有关。采用流式细胞术检测SLE患者B细胞上补体受体和调节蛋白的表达,以及体内或体外AP激活后C3片段的沉积情况。对于部分研究患者,我们证实了其B细胞上CR1和CR2表达降低,并显示在存在同源正常血清的情况下,CR2低表达与体外AP激活降低之间具有一致性。此外,与正常B细胞相比,SLE患者的B细胞与红细胞一样,体内沉积的C3dg水平升高,但C3b片段水平未升高。SLE患者的红细胞无法抑制同源血清中B细胞的体外AP激活。最后,我们证明了SLE疾病活动指数(SLEDAI)与SLE B细胞上补体受体2(CR2)的表达呈负相关。因此,检测B细胞上的CR2可能成为评估SLE活动度的一项额外实验室指标。