Idiopathic peripheral pulmonary artery stenosis: an unusual cause of ventilation-perfusion mismatch.

Idiopathic peripheral pulmonary artery stenosis is a rare cause of ventilation-perfusion mismatch in adults. We report a 39-yr-old man with this entity. Pulmonary scintigraphy demonstrated findings indistinguishable from pulmonary embolism, and pulmonary angiography was necessary for accurate diagnosis.