Robert T L, Varella L, Meguid M M
Department of Surgery, University Hospital, SUNY Health Science Center 13210.
Nutrition. 1994 Nov-Dec;10(6):551-5; quiz 556-7.
A patient with acute intermittent porphyria is presented to emphasize the relevance of nutrition in its management. Clinical manifestations, diagnosis of acute intermittent porphyria, simplified heme biosynthetic pathway, the glucose effect, and the rationale for giving nutritional therapy for acute intermittent porphyria are discussed.
本文介绍了一名急性间歇性卟啉病患者，以强调营养在其治疗中的相关性。讨论了急性间歇性卟啉病的临床表现、诊断、简化的血红素生物合成途径、葡萄糖效应以及给予急性间歇性卟啉病营养治疗的基本原理。
