Sataloff R T, Frattali M A, Myers D L
Department of Otolaryngology-Head and Neck Surgery, Thomas Jefferson University, Philadelphia, Pennsylvania, USA.
Ear Nose Throat J. 1995 Apr;74(4):244-6, 248-56.
Neuromas of the facial nerve are uncommon tumors. The majority of cases involve the intratemporal and parotid areas. Since their description in 1930, there have been only 26 cases of intracranial facial neuroma reported in the world literature. Of these, 19 involved the middle cranial fossa, and only seven tumors extended into or originated in the posterior cranial fossa. In this location, the seventh nerve is surrounded by a very delicate and thin arachnoid casing. Thus, although these tumors are encapsulated, there is usually no obvious plane of separation between the tumor and perineurium. As a result, the seventh nerve has been sacrificed routinely. Two patients with posterior fossa facial neuromas underwent total tumor removal with a new surgical technique permitting preservation of the nerve fascicles via a translabyrinthine approach. Each patient has good recovery of seventh nerve function with no evidence of recurrence six and nine years later, respectively. Leaving the nerve fascicles intact appears to result in good reinnervation following total tumor removal. The potential value of this technique is best considered in the context of diagnostic and therapeutic options for facial neuromas in general. Neurotologists should find this a useful addition to their surgical armamentarium for selected cases.
面神经神经瘤是罕见肿瘤。大多数病例累及颞骨内和腮腺区域。自1930年其被描述以来,世界文献中仅报道了26例颅内面神经瘤。其中,19例累及中颅窝,仅有7例肿瘤延伸至后颅窝或起源于后颅窝。在此部位,面神经被一层非常薄且脆弱的蛛网膜包裹。因此,尽管这些肿瘤有包膜,但肿瘤与神经束膜之间通常没有明显的分隔平面。结果,面神经通常被牺牲。两名后颅窝面神经瘤患者采用一种新的手术技术,通过经迷路入路切除了全部肿瘤,并保留了神经束。两名患者的面神经功能均恢复良好,分别在术后6年和9年无复发迹象。在完全切除肿瘤后,保留神经束似乎能实现良好的神经再支配。一般而言,该技术的潜在价值最好结合面神经瘤的诊断和治疗选择来考虑。对于特定病例,神经耳科医生会发现这是其手术手段中的一项有用补充。