Saatci I, Coskun M, Boyvat F, Cila A, Gürgey A
Department of Diagnostic Radiology, Hacettepe University Hospital, Ankara, Turkey.
Pediatr Radiol. 1995;25(1):31-3. doi: 10.1007/BF02020839.
Peliosis is an uncommon condition characterized by multiple-blood-filled cavities mostly involving the liver. Although the etiology is unknown the condition may be associated with several disease states and medications. We report the MR findings of peliosis hepatis in a patient with Fanconi anemia who had been treated with anabolic androgenic steroids for 3 years. The MR examination of the upper abdomen was performed on a 0.5 T system. The signal intensity of the right lobe of the liver was diffusely increased in all sequences. Within the enlarged liver, multiple foci of brighter signal were seen involving both right and left lobes. The lesions showed contrast enhancement. A cystic cavity with an enhancing rim was seen representing a haematoma cavity. The spleen was spared the patient died of sepsis and the postmortem examination confirmed the diagnosis of peliosis hepatis.
肝紫癜是一种罕见病症,其特征为多个充满血液的腔隙,主要累及肝脏。尽管病因不明,但该病症可能与多种疾病状态及药物有关。我们报告了一名患有范可尼贫血的患者的肝紫癜磁共振成像(MR)表现,该患者接受合成代谢雄激素类固醇治疗达3年。上腹部的MR检查在一台0.5T系统上进行。肝脏右叶在所有序列中的信号强度均弥漫性增加。在增大的肝脏内,可见多个信号增强的病灶,累及左右两叶。这些病变显示有对比增强。可见一个有强化边缘的囊性腔隙,代表血肿腔。脾脏未受累,患者死于败血症,尸检证实为肝紫癜。