韦格纳氏脂膜炎与自身免疫性疾病：一例报告

J Clin Pathol. 1976 Feb;29(2):144-9. doi: 10.1136/jcp.29.2.144.

A case is described of Weber-Christian panniculitis accompanied by a gammaglobulin disturbance which preceded by five years the diagnosis of an autoimmune hepatitis and pancytopenia. Also associated was the onset of diabetes mellitus, found at necropsy to be related to pancreatic islet amyloid deposition. This case reinforces the view that Weber-Christian panniculitis may be an adipose response to a variety of immunological stimuli.

描述了一例伴有γ球蛋白紊乱的韦氏-克里斯蒂安脂膜炎，该脂膜炎在自身免疫性肝炎和全血细胞减少症诊断前五年出现。还伴有糖尿病的发生，尸检发现其与胰岛淀粉样沉积有关。该病例强化了这样一种观点，即韦氏-克里斯蒂安脂膜炎可能是对多种免疫刺激的脂肪反应。