Morita K, Shimizu J, Kamesui T, Watanabe Y, Nonomura A, Kita K
Department of Surgery, Kanazawa University School of Medicine, Japan.
Nihon Kyobu Geka Gakkai Zasshi. 1994 Oct;42(10):1949-52.
Swyer-James syndrome was usually diagnosed on the past history and the radiologic features, and almost all the cases were followed by the conservative therapy. Therefore, the examination of the pathologic features was rare. We recently experienced a patient with Swyer-James syndrome, who had a history of respiratory infection from his childhood onward and whose chest radiograph revealed hyperlucency of the right lower lung field. A standard right middle and lower lobectomy was performed. Histological examination of the resected specimens revealed hypoplasia of alveoli and pulmonary artery.
斯怀尔-詹姆斯综合征通常根据既往病史和影像学特征进行诊断，几乎所有病例均采用保守治疗。因此，对其病理特征进行检查的情况较为罕见。我们最近遇到一名患有斯怀尔-詹姆斯综合征的患者，他自幼就有呼吸道感染病史，胸部X光片显示右下肺野透亮度增加。实施了标准的右中、下叶切除术。对切除标本的组织学检查显示肺泡和肺动脉发育不全。
