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晚期白点状视网膜变性患者无色素沉着。

No pigment deposition in a patient with advanced retinitis punctata albescens.

作者信息

Fujii M, Hayasaka S

机构信息

Department of Ophthalmology, Shimane Medical University, Izumo, Japan.

出版信息

Ophthalmologica. 1994;208(6):339-41. doi: 10.1159/000310535.

DOI:10.1159/000310535
PMID:7845653
Abstract

A 51-year-old woman had had night blindness since childhood and a progressive visual field defect. She was the product of a consanguineous marriage. The patient also exhibited numerous whitish-yellow punctate spots with no pigment deposition in her fundi, nonrecordable electroretinographic responses after 30 min of dark adaptation, and constricted visual fields bilaterally. We believe that our patient may be a case of retinitis punctata albescens without pigment.

摘要

一名51岁女性自幼患有夜盲症且视野进行性缺损。她是近亲结婚的后代。该患者眼底还出现大量白黄色点状斑点,无色素沉着,暗适应30分钟后视网膜电图反应无法记录,双侧视野狭窄。我们认为我们的患者可能是一例无色素性点状视网膜病变。

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