Miyashita T, Imamura T, Ishikawa Y, Okinaga K, Kunii O, Miyashita H
Second Department of Internal Medicine, Teikyo University School of Medicine, Tokyo.
Intern Med. 1994 Nov;33(11):692-6. doi: 10.2169/internalmedicine.33.692.
We present a patient with primary retroperitoneal synovial sarcoma which showed a monophasic fibrous pattern, the fourth such case to be described, and a review of the literature. Synovial sarcoma cells in the present case were stained positive for cytokeratin and epithelial membrane antigen (EMA), of which histology was differentiated from other spindle cell sarcoma with similar light microscopic features. Retroperitoneal synovial sarcoma is usually treated surgically, however only one of 16 cases identified in the literature survived five years after resection. Due to the high fatality rate, physicians should be alerted to the possibility of this disorder in the differential diagnosis of an abdominal mass.
我们报告了一例原发性腹膜后滑膜肉瘤患者，该肿瘤表现为单相纤维型，这是第四例被描述的此类病例，并对相关文献进行了综述。本例滑膜肉瘤细胞细胞角蛋白和上皮膜抗原（EMA）染色呈阳性，其组织学特征与其他具有相似光镜特征的梭形细胞肉瘤不同。腹膜后滑膜肉瘤通常采用手术治疗，然而，文献中报道的16例病例中只有1例在切除术后存活了5年。由于死亡率高，医生在腹部肿块的鉴别诊断中应警惕这种疾病的可能性。
