Brown E W, Megerian C A, McKenna M J, Weber A
Department of Radiology, Harvard Medical School, Massachusetts Eye and Ear Infirmary, Boston 02114.
AJR Am J Roentgenol. 1995 Mar;164(3):679-82. doi: 10.2214/ajr.164.3.7863893.
Lichtenstein [1] in 1938 coined the term fibrous dysplasia to describe a disorder characterized by the progressive replacement of normal bone elements by fibrous tissue. Histopathologically, these lesions consist of an abnormal proliferation of fibrous elements intermixed with haphazardly arranged trabeculae of woven bone. The disease can involve any bone in the body. In the head and neck, the skull and facial bones are involved in 10-25% of cases of monostotic fibrous dysplasia and in 50% of the polyostotic variety. Involvement of the temporal bone, however, is relatively rare, and only 53 cases have been reported. The three major radiographic classifications of fibrous dysplasia are pagetoid, sclerotic, and cystic. Any of these types may involve the temporal bone and related structures, including the external canal, middle ear, jugular foramen, or, rarely, the otic capsule. In this essay, we illustrate the radiographic features of the disease based on our experience with seven cases, seen at our institution since 1977, of fibrous dysplasia involving the temporal bone.
1938年，利希滕斯坦[1]创造了“骨纤维异常增殖症”一词，用于描述一种以纤维组织逐渐取代正常骨成分的疾病。在组织病理学上，这些病变由纤维成分的异常增殖组成，其间夹杂着杂乱排列的编织骨小梁。该疾病可累及身体的任何骨骼。在头颈部，单发性骨纤维异常增殖症病例中，颅骨和面部骨骼受累的比例为10% - 25%，而在多骨性骨纤维异常增殖症病例中这一比例为50%。然而，颞骨受累相对少见，仅有53例相关报道。骨纤维异常增殖症的三种主要影像学分类为骨炎样、硬化型和囊肿型。这些类型中的任何一种都可能累及颞骨及相关结构，包括外耳道、中耳、颈静脉孔，或极少情况下累及耳囊。在本文中，我们根据自1977年以来在我们机构所见的7例累及颞骨的骨纤维异常增殖症病例的经验，阐述该疾病的影像学特征。
