Matute J A, Encinas A, Hernández J M, Varela G, Berchi F J, Vilariño A
Servicio de Cirugía Pediátrica, Hospital Materno-Infantil 12 de Octubre, Madrid.
Cir Pediatr. 1994 Oct;7(4):157-63.
Congenital tracheal stenosis is a rare condition with a high mortality. In a 12-year period, 5 cases (ages 5 days to 4 years) with this anomaly were treated. 4 were corrected, the operative repair consisted of segmental resection and anastomosis in one patient, and rib-cartilage tracheoplasty in the other three. The other patient died 12 days after bronchoscopy without attempt of surgical correction. Two patients died during or just after surgery, both of them presenting a similar clinical course consisting on severe air trapping, mechanical pulmonary hypertension and low cardiac output. Long-term follow-up of the survivors is satisfactory.
先天性气管狭窄是一种罕见但死亡率很高的疾病。在12年期间，共治疗了5例患有这种异常的患者（年龄从5天至4岁）。4例得到了矫正，其中1例患者的手术修复包括节段性切除和吻合术，另外3例采用肋软骨气管成形术。另1例患者在支气管镜检查后12天死亡，未尝试进行手术矫正。2例患者在手术期间或刚手术后死亡，他们都呈现出类似的临床过程，包括严重的气体潴留、机械性肺动脉高压和低心输出量。幸存者的长期随访情况良好。
