Weber T R, Connors R H, Tracy T F
Department of Surgery, St. Louis University School of Medicine, Missouri.
Ann Surg. 1991 Jan;213(1):70-4. doi: 10.1097/00000658-199101000-00012.
Cogenital tracheal stenosis with unilateral pulmonary agenesis is a rate and frequent fetal combination. In an 8-year period, 5 infants (ages 2 to 6 months) with these anomalies were treated. The presenting signs and symptoms consisted of wheezing, stridor, and tachypnea and included frank respiratory failure requiring emergency therapy in several patients. The operative repair consisted of segmental resection and anastomosis in one patient, and rib-cartilage tracheoplasty in the other four. Two infants died, one of cerebral hypoxia, and the other of aortotracheal fistula. Long-term follow-up in the three survivors is satisfactory.
先天性气管狭窄合并单侧肺不发育是一种罕见的胎儿组合畸形。在8年期间，对5例患有这些异常的婴儿（年龄2至6个月）进行了治疗。主要体征和症状包括喘息、喘鸣和呼吸急促，部分患者出现需要紧急治疗的明显呼吸衰竭。手术修复包括1例患者行节段性切除和吻合术，另外4例患者行肋软骨气管成形术。2例婴儿死亡，1例死于脑缺氧，另1例死于主动脉气管瘘。3名幸存者的长期随访情况良好。
