Tsang T M, Tam P K, Chamberlain P
Nuffield Department of Surgery, John Radcliffe Hospital, Oxford, England.
J Pediatr Surg. 1994 Dec;29(12):1582-3. doi: 10.1016/0022-3468(94)90224-0.
The authors report the first case of antenatally diagnosed choledochal cyst having evidence of early fetal bile drainage and complete obliteration of the distal bile duct. This disputes the traditional hypothesis of reflux of pancreatic enzymes and supports the recent theory of primary obstruction as the etiologic cause of choledochal cyst. Coexisting congenital hypothyroidism and pulmonary stenosis had not been reported previously.
作者报告了首例产前诊断的胆总管囊肿病例，该病例有早期胎儿胆汁引流及远端胆管完全闭塞的证据。这对胰酶反流的传统假说提出了质疑，并支持了原发性梗阻作为胆总管囊肿病因的最新理论。此前尚未报道过并存先天性甲状腺功能减退症和肺动脉狭窄的情况。
