Matsumoto J Y, Caviness J N, McEvoy K M
Department of Neurology, Mayo Clinic and Foundation, Rochester, MN 55905.
Neurology. 1994 Oct;44(10):1952-5. doi: 10.1212/wnl.44.10.1952.
We studied the EMG response to loud noise in eight patients with stiff-man syndrome (SMS). Audiogenic muscle jerks originated in the acoustic startle reflex. Patients demonstrated excessive, poorly habituating motor activity predominantly in axial and leg muscles. Exaggerated startle in SMS probably reflects segmental hyperexcitability of axial and lumbar spinal motor neurons.
我们研究了8例僵人综合征(SMS)患者对巨响的肌电图反应。听觉性肌阵挛起源于听觉惊吓反射。患者主要在轴性和腿部肌肉表现出过度的、难以习惯化的运动活动。SMS中夸张的惊吓反应可能反映了轴性和腰段脊髓运动神经元的节段性过度兴奋性。